临床实践中弥漫性肺疾病诊断

细支气管炎性间质性肺疾病(RBILD)? 脱屑性间质性肺炎(DIP)? 隐源性机化性肺炎(COP)? 急性间质性肺炎(AIP)Р2 少见的特发性间质性肺炎? 特发性淋巴细胞性间质性肺炎(idiopathic LIP)? 特发性胸膜肺纤维弹性组织增生症(idiopathic pleuropulmonary fibroelastosis PPFE)Р3 未能分类的特发性间质性肺炎РDiifuse Parenchymal Lung DiseaseРGranulomatous?DPLD e.g.?SarcoidosisРIdiopathic interstitial ?pneumonia?(IIPs)РDPLD of knowa?cause e.g. Drugs?or association e.g.?collagen vascular diseaseРOther foms of DPLD? e.g. LAM,HX etc.РNON-familial Familial? (>80%) (2-20%)РIdiopathic pulmonary fibrosis ?Idiopathic nonspecific interstitial pneumoniaРSmoking-relatedРAcute/subacute ?FibrosingРChronic FibrosingРRespiratory bronchiolitis intrestitial lung disease?Desquamative intrestitial pneumoniaРanizing pneumonia?Acute interstitial pneumoniaР临床诊断困惑Р临床诊断的困惑РATS/ERS 建议病理诊断用类型(Pattern),而非用病理诊断取代临床放射诊断。Р临床Р病理РDPLD诊断Р影像学